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Name | Dermatofibrosarcoma protuberans over an anterior abdominal wall: A rare case report with brief review of literature |
Description | Case report:- Sneha S. Desale1, Nandkumar V. Dravid2, Dhiraj B. Nikumbh3*, Dhananjay V. Newadkar4 & Yogesh R. Tayade5 Assistant lecturer1, Prof & HOD2, Associate professor3, Professor4, Assistant lecturer5, Department of Pathology, JMF’s ACPM Medical college and hospital, Dhule, Maharashtra, India.
Abstract:- Dermatofibrosarcoma Protuberans (DFSP) is a rare, indolent,low grade soft tissue sarcoma with properties of progressive and locally infiltrative growth. Less than 5% of sarcomas appear as primary abdominal wall tumors. DFSP mostly occur over the trunk or proximal extremities. DFSP accounts for <0.01% of all malignancies and <0.1% of all the cutaneous neoplasms. DFSP over an anterior abdominal wall is a rare clinical entity. Herein, we present a case of DFSP over anterior abdominal wall in a 35 year old male, which was diagnosed on histopathology and confirmed on immunohistochemistry. DFSP is a rare dermal malignancy with a propensity to be locally aggressive but rarely metastatic. Hence proper histopathological diagnosis is always warranted in such rare tumor.
Keywords:- Soft tissue sarcoma, Dermatofibrosarcoma Protuberans,Abdominal wall.
References:- 1.Weiss SW, Goldblum JR: Fibrohistiocytic tumors of intermediate malignancy. In: Weiss SW, Goldblum JR (ed) Enzinger & Weiss’s soft tissue tumours. 5th editions. Mosby Elsevier pub. 2008:371-383. 2.Dragoumis DM, Katsohi LAK, Amplianitis DC, Tsiftsoglou AP. Late local recurrence of Dermatofibrosarcoma Protuberans in the skin of female breast. World Journal of surgical oncology. 2010,8: 48. 3.Makkar M, Singh DP, Rana A, Madan M. Recurrent dermatofibrosarcoma protuberans : A continuing problem. Indian Dermatol online. 2013;4:68-9. 4.Lee SJ, Mahoney MC, Shaughnessy E: Dermatofibrosarcoma protuberns. A clinicopathological study of 19 cases & review of world literature. Scand J Plast Reconstr Surg. 1983;17:247-52. 5.Stojadinovic A, Hoos A, Karpoff HM, Leung DH, Antonescu CR, Brennan MF, et al. Soft tissue tumours of the abdominal wall: analysis of disease pattern and treatment. Arch Surg. 2001;136:70-9. 6.Asuquo ME, Umoh MS, Ebughe G. Dermatofibrosarcoma protuberans:case reports. Annals of African Medicine. 2007:6(2):80-3. 7.Sinha VD, Dharkar SR, Katra GS. Dermatofibrosarcoma protuberns of scalp: a case report. Neurol India. 2001;49:81-3. 8.Park TH, Seo SW, Kim JK, Chang CH. Reconstructive challenge of dermatofibrosarcoma protuberans in the female breast. World Journal of Surgical Oncology. 2011;9:1. 9.Shrimali R,,Gang L,Setia V,Jain S.DFSP.CT finding in dermatofirbosarcoma protuberns.a rare skin tumor.Indian J Radil Imaging.2002;12:357-8. 10.Kiuru-Kuhlefelt S, El-Rifai W, Fanburg-Smith J,Kere J, Meinttinen M, Knuutila S. Concomitant DMA copy number amplification at 17q and22q in dermatofibrosarcoma protuberans. Cytogenet Cell Genet.2001;92:192-5.
Copyright © 2013 Nikumbh et al.. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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